Lymphangiomatosis na Lymph System

Lymphangiomatosis bụ ọrịa nke ọtụtụ ọrịa ara (lymphangiomas) ma ọ bụ cysts na-eto eto n'ime usoro lymph nke ahụ. Ọ bụ ezie na ụbụrụ ndị a adịghị emerụ ahụ, ha na-awakpo anụ ahụ ma kpatara mgbu, ike iku ume, na ọtụtụ mgbaàmà ndị ọzọ dabere na ebe ha na-eme. Lymphangiomas nwere ike itolite n'ime ọkpụkpụ, anụ ahụ jikọtara, na akụkụ ahụ nke ahụ, ma ha nwere ike igbochi, mpepịa, ma ọ bụ bibie anụ ahụ.

Ihe na-akpata lymphangiomatosis ka amarabeghị.

A na-ahụkarị Lymphangiomatosis na ụmụ ọhụrụ na ụmụntakịrị mana ha nwere ike ime n'oge ọ bụla. Ọ na-emetụta ma ụmụ nwoke ma nwanyị nke agbụrụ niile. Ebe ọ bụ na lymphangiomatosis bụ obere ma sie ike ịchọpụta nke ọma, ọ maghị kpọmkwem mmadụ ole na ole na-emetụta ya n'ụwa nile.

Mgbaàmà

Ihe mgbaàmà nke lymphangiomatosis na-adabere na ebe etuto ahụ na-etolite n'ime ahụ.

N'ime oge, otu ma ọ bụ karịa ọkpụkpụ nwere ike dochie anya anụ lymphangioma, nke a maara dịka ọrịa Gorham. Lymphangiomas anaghị eto ụbụrụ n'ihi na usoro lymph adịghị aba n'ime ya.

Nchoputa

Nchoputa nke lymphangiomatosis dabeere na mgbaàmà na ọnụnọ nke ọtụtụ lymphangiomas n'ime ahụ. CT (nke a na-atụle entergraphy) na iṅomi na ntanetị nke resonance magnet (MRI) ejiri iji nyochaa ọrịa ahụ. A na - ewepụta ụdị nsị (biopsy) iji nyere aka gosi na etuto ahụ bụ lymphangiomas.

Ọgwụgwọ

Lymphangiomatosis ji nwayọọ nwayọọ na-aka njọ n'oge. Ka etuto ahụ na-etolite, ha nwere ike ịkpata mgbaàmà ndị siri ike, ụfọdụ n'ime ha nwere ike ibute egwu ndụ, dị ka ịme ka mmiri nakọtara na akpa ume nke na-egbochi iku ume. A na-ewepu mgbochi ụbụrụ nke ọma, ma ụfọdụ etuto ahụ nwere ike isi ike iwepụ kpam kpam ma ọ bụrụ na ha agbasaa. Otu ọgwụ a na-akpọ Intron A (interferon alfa), ọgwụgwọ, ma ọ bụ ọgwụ radiation nwere ike inye aka n'ịgwọ ọrịa ahụ. Ngwọta ndị ọzọ ma ọ bụ surgeries nwere ike inye aka n'ịkwụsị ụfọdụ mgbaàmà ma ọ bụ nsogbu nke lymphangiomatosis kpatara. Dịka ọmụmaatụ, enwere ike ịtinye tube n'ime obi (thoracentesis) iji kpochapụ mmiri a gbakọtara, ma ọ bụ ịwa ahụ nwere ike ime na nkedo iji wepụ ihe irighiri akwara.

Isi mmalite:

> "Banyere Lymphangiomatosis." Lymphangiomatosis & Gorham's Disease Alliance. 06 Sep 2007. Lymphangiomatosis & Gorham's Disease Alliance.

> Marom, Edith, Cesar Moran, & Reginald Munden. "Na-emepụta Lymphangiomatosis." American Journal of Roentgenology 182 (2004): 1068.

> Rostom, A Y. "Ọgwụgwọ nke thoracic lymphangiomatosis." Nchịkọta Ọrịa nke Ụmụaka 83 (2000): 138-139.