Kemgbe ọtụtụ afọ, a na-ejikọta muscular dystrophy na ụmụ Jerry. Nke ahụ bụ, Jerry Lewis gbara ya gburugburu site na ụmụaka n'oge nkuzi Muscular Dystrophy Association's Day Labor Day. Site n'afọ 1966 rue 2010, Jerry Lewis kwadoro teleton a kwa afọ iji baara ndị nwere musy dystrophy uru. Dystrophy (Muscular dystrophy) na-anọchi anya otu ìgwè ọrịa ahụ tara.
Telethon gara na Lewis site na 2010 ruo n'afọ 2014, na-agwụsị na 2015.
Ọ bụ ezie na telethon kwa afọ, muscular dystrophy - ụdị nke itoolu - ka dị. Ụdị nke itoolu bụ ndị a.
1. Duchenne Muscular Dystrophy
Dystrophy muscular duchenne (DMD) bụ ụdị ụmụaka nke kachasị na-adị na nwata, dystrophy, na mgbaàmà na-amalite site n'agbata afọ 2 ruo 6. DMD kacha emetụta ụmụaka. Ụmụ agbọghọ nwere ike iburu ọnọdụ ahụ ma nwee ike imetụ n'ahụ. Ihe ịrịba ama mbụ nke DMD nwere ike ịgụnye ụda ugboro ugboro, ihe isi ike na-ebili site na ịnọdụ ala ma ọ bụ dina ala, na ije ije dị ka ọnụ. Nwatakiri nwere DMD nwekwara ike igosi na enwere ike ikpo nwa.
Ọrịa ahụ na-aga n'ihu nke nta nke nta, mana enyemaka enyemaka ga-adịcha mkpa - na-eduga n'oche nkwagharị. Ka ahụ ahụ na-arịwanye elu nke nta, nsogbu na-eku ume na-etolite. Nke a nwere ike ibute ọrịa respiratory dịka pneumonia, nke nwere ike isiri ndị mmadụ ike na DMD ịlụ agha.
N'ihi ọganihu na nchọpụta na teknụzụ, atụmanya ndụ maka DMD amụbawo n'ime mmalite 30s.
2. Becker Dystrophy Muscular
Becker muscular dystrophy dị nnọọ ka DMD, ma e wezụga na ihe mgbaàmà nke Becker MD nwere ike ịpụta mgbe ọ dị na nwata - ruo ruo oge dịka 25. Ọ bụ ezie na yiri DMD, ihe mgbaàmà nke Becker MD ọganihu karịa nke DMD.
3. Dystrophy Muscular Congenital
Congenital muscular dystrophy na-anọchite anya ìgwè nke ọkpụkpụ muscle nke dị n'oge ọmụmụ. Ụdị MD a nwere ike imetụta ma ụmụ nwoke ma ụmụ agbọghọ. Achọpụtaghị ụdị mkparị niile. Otu ụdị, Fukuyama congenital muscular dystrophy, na-akpata adịghị ike dị ukwuu nke ahụ ike na aka na ike na-agụnye nkwonkwo nkwekọrịta, nsogbu uche na okwu, yana ihe ijide .
4. Emery-Dreifuss Muscular Dystrophy
Dystrophy muscular-Emery-Dreifuss bụ ụdị nke MD na-adịghị adịkarị na-emetụta ụmụ nwoke. Ụdị a na-eme nke ọma. Otú ọ dị, n'adịghị ka DMD, nkwekọrịta - nkwụsị ahụ ike - nwere ike ịpụta na mbido. Ọdịdị nkwonkwo ahụ ike n'ozuzu ya dịkwa obere karịa nke DMD. Nsogbu obi obi tara aka na Emery-Dreifuss MD nwere ike ịchọ onye na-arụ ọrụ.
5. Dystrophy Muscular nke Na-ejikarị Aka
Limb-girdle muscular dystrophy amalite na nwata ma ọ bụ na-eto eto afọ nke abụọ genders. Ọrịa ahụ na-akpata adịghị ike anụ ahụ nke na-amalite na ọdịda, na-ebuga n'ubu, ma gbasaa n'ime ogwe aka na ụkwụ. Ọrịa ahụ na-aga n'ihu jiri nwayọọ nwayọọ ma na-eduga ná nsogbu ịga ije.
6. Dystrophy Muscular Facioscapulohumeral
Facioscapulohumeral muscular dystrophy (FSH MD) na-amalite n'oge uto ma ọ bụ na-eto eto ma na-emetụta ma ụmụ nwanyị.
FSH MD na-emetụta ahụ mgbochi ihu ("facio-"), akpa ubu ("scapulo-"), na ogwe aka elu ("ọnụ ọgụgụ"). Ndị nwere FSH MD nwere ubu na-aga n'ihu, na-eme ka o sie ike ibuli aka ha n'elu isi ha. Adịghị ike nke ahụ na-aga n'ihu n'ahụ ahụ ka ọrịa ahụ na-aga n'ihu. FSH MD nwere ike ịmalite site n'ịdị nwayọọ ruo n'oké njọ. N'agbanyeghị ahụ ike na-aga n'iru, ọtụtụ ndị nwere FSH MD ka nwere ike ịga ije.
7. Myotonic Muscular Dystrophy
Myotonic muscular dystrophy (ọrịa Steinert) bụ ụdị nkịtị nke okenye muscular dystrophy. Ụdị nke muscular dystrophy na-amalite site n'adịghị ike nke ahụ na ihu ma na-agafe ụkwụ na aka.
Myotonic MD na - ebute ụkwara na - eme ka mgbochi dị ogologo (dị ka spasms) - mgbaàmà nke na - eme na ụdị MD a. Myotonic MD na-emetụta usoro nhụjuanya bụ isi, obi, traktị na-egbu nri, anya, na endocrine glands . Ọ na-aga n'ihu nwayọ, na ọnụ ọgụgụ nke adịghị ike ahụ ike na-adịgasị iche site na nwayọọ ruo oke. Otu nwanyị nwere MD myotonic nwere ike ịmị nwa ọhụrụ nke nwere ọrịa ahụ.
8. Dystrophy Muscular Oculopharyngeal
Ogulopharyngeal muscular dystrophy na-amalitekarị n'afọ nke anọ ma ọ bụ ise nke ndụ. Ịda anya eyelid bụ ihe ịrịba ama mbụ nke ụdị dystrophy a. Ọnọdụ ahụ na-enwe ọganihu n'adịghị ike ọdịdị ihu na ike ịnwe. Ịwa ahụ nwere ike belata iwepụ nsogbu ma gbochie nkwụsị na nkwonkwo.
9. Dystrophy Muscular Distal
Dystrophy muscular dị iche na-agụnye ọtụtụ ọrịa ndị na-amalite na okenye ma nwee mgbaàmà yiri nke adịghị ike aka, aka, ụkwụ ukwu, na ụkwụ. Ọrịa ndị a - tinyere nchịkwa Welander, Markesbury-Griggs, Nonaka, na Miyoshi - adịghị njọ ma na-agụnye uru ahụ karịa obere ụdị musy dystrophy. Ụdị dị iche iche na-emetụta ma ndị nwoke ma ndị nwanyị.
Isi mmalite:
Muscular Dystrophy Association USA.
Newsweek. The musical dystrophy telethon ugbu a bụ naanị ebe nchekwa (2015).